Metabolomics & Nutrition COQ10

Coenzyme Q10 (Ubiquinone).

Quantitative measurement of ubiquinone (coenzyme Q10) from a dried blood spot. Performed by LC-MS/MS for assessment of mitochondrial function and antioxidant capacity.

Quick Reference
Method
LC-MS/MS
Sample Types
DBS
Analyte

Ubiquinone (CoQ10)

Turnaround

3–5 working days

View Sample Report Enquire About This Test

What does this test assess?

This method quantifies coenzyme Q10 (ubiquinone) from a dried blood spot. CoQ10 is an essential component of the mitochondrial electron transport chain and a potent endogenous antioxidant. Its measurement is important in evaluating mitochondrial function, statin-related myopathy risk, and supplementation efficacy.

Clinical indications include:

  • Assessment of mitochondrial dysfunction in primary CoQ10 deficiency syndromes
  • Monitoring of CoQ10 depletion during statin therapy (HMG-CoA reductase inhibitors share the mevalonate pathway with CoQ10 biosynthesis)
  • Evaluation of myopathy, fatigue, and exercise intolerance potentially related to CoQ10 insufficiency
  • Cardiovascular risk assessment — CoQ10 is concentrated in myocardial tissue
  • Assessment in neurodegenerative conditions including Parkinson's disease and Huntington's disease
  • Monitoring supplementation efficacy in clinical and wellness settings

About Coenzyme Q10

Coenzyme Q10 (also known as ubiquinone-10) is a lipid-soluble benzoquinone that is synthesised endogenously via the mevalonate pathway — the same biosynthetic route used for cholesterol production. It is present in virtually all human cells, with the highest concentrations found in organs with high metabolic demand: the heart, liver, kidneys, and skeletal muscle.

Dual role

Essential for both mitochondrial ATP production and lipid antioxidant defence

Statin interaction

Statins inhibit the mevalonate pathway, reducing endogenous CoQ10 synthesis by up to 40%

Age-related decline

Tissue CoQ10 levels peak around age 20 and decline progressively thereafter

In the mitochondrial electron transport chain, CoQ10 shuttles electrons from complexes I and II to complex III, making it indispensable for oxidative phosphorylation and ATP generation. In its reduced form (ubiquinol), it also functions as a potent lipid-phase antioxidant, protecting cell membranes and circulating lipoproteins from peroxidation.

Primary CoQ10 deficiency is a group of autosomal recessive disorders caused by mutations in genes involved in ubiquinone biosynthesis. Clinical presentations range from severe infantile multisystem disease to isolated myopathy or cerebellar ataxia. Early diagnosis and supplementation can significantly improve outcomes in these conditions.

Secondary deficiency is far more common and is most frequently associated with statin therapy. Since statins inhibit HMG-CoA reductase — the rate-limiting enzyme in both cholesterol and CoQ10 biosynthesis — patients on long-term statin treatment may experience reduced CoQ10 levels, potentially contributing to statin-associated myopathy and fatigue. Monitoring CoQ10 in these patients can guide supplementation decisions.

Analytical technique

Coenzyme Q10 is extracted from a dried blood spot and quantified by isotope-dilution LC-MS/MS using a deuterium-labelled internal standard (CoQ10-d9). The method provides high sensitivity and specificity, accurately measuring total ubiquinone without interference from ubiquinol or other quinone species.

LC-MS/MS is the preferred analytical platform for CoQ10 due to its ability to resolve ubiquinone from structurally related compounds and achieve the low quantification limits required for clinical interpretation, particularly in deficiency states.

Sample information

The DBS matrix provides a convenient and stable collection format for CoQ10 measurement. CoQ10 in dried blood spots is stable at ambient temperature when protected from light, making it suitable for remote collection, postal transit, and population screening programmes.

Testing process

From enquiry to results in a few simple steps — no clinic visit required.

1
Get in touch
Contact us to discuss your testing requirements
2
Collect your sample
Simple finger-prick onto a dried blood spot card — at home or in clinic
3
Post to our lab
DBS cards are stable at room temperature — ship by regular post worldwide
4
Receive results
Results delivered within 3–5 working days of sample receipt

Where this test is available

This test is available to healthcare professionals, wellness brands, clinics, and research institutions worldwide. We currently serve partners in:

  • Europe (EU & non-EU)
  • United Kingdom
  • Asia & Southeast Asia
  • Australia & New Zealand
  • United States

Whether you need testing services for your patients, white-label kits for your brand, or method transfer to your own laboratory — get in touch to discuss how we can work together.

Literature

  1. Littarru GP, Tiano L. “Bioenergetic and antioxidant properties of coenzyme Q10: recent developments.” Molecular Biotechnology, 2007, 37(1):31–37. 10.1007/s12033-007-0052-y
  2. Desbats MA, Lunardi G, Doimo M, Trevisson E, Salviati L. “Genetic bases and clinical manifestations of coenzyme Q10 deficiency.” Journal of Inherited Metabolic Disease, 2015, 38(1):145–156. 10.1007/s10545-014-9749-9
  3. Banach M et al. “Statin therapy and plasma coenzyme Q10 concentrations — a systematic review and meta-analysis.” Pharmacological Research, 2015, 99:329–336. 10.1016/j.phrs.2015.07.012
  4. Molyneux SL et al. “Coenzyme Q10: an independent predictor of mortality in chronic heart failure.” Journal of the American College of Cardiology, 2008, 52(18):1435–1441. 10.1016/j.jacc.2008.07.044
  5. Crane FL. “Biochemical functions of coenzyme Q10.” Journal of the American College of Nutrition, 2001, 20(6):591–598. 10.1080/07315724.2001.10719063

Frequently Asked Questions

What is Coenzyme Q10?

Coenzyme Q10 (also known as ubiquinone) is a fat-soluble compound found in virtually every cell in the body, with the highest concentrations in organs with high metabolic demand such as the heart, liver, and kidneys. It plays a dual role: it is essential for ATP production in the mitochondrial electron transport chain, and it functions as a potent lipid-phase antioxidant protecting cell membranes from oxidative damage. Masdiag measures CoQ10 as ubiquinone from a dried blood spot by LC-MS/MS.

Why should I test my CoQ10 levels?

CoQ10 levels decline naturally with age and can be significantly depleted by statin medications, which inhibit the same biosynthetic pathway used to produce both cholesterol and CoQ10. Low CoQ10 has been linked to fatigue, muscle pain, exercise intolerance, and cardiovascular dysfunction. Testing provides an objective measurement to guide supplementation decisions, particularly for long-term statin users.

How is the sample collected?

The test uses a simple finger-prick to collect a few drops of blood onto a dried blood spot (DBS) card. You can do this at home or in a clinic — no venous blood draw is needed. The DBS card is stable at room temperature when protected from light and can be posted to our laboratory by regular mail.

How long does it take to get results?

Results are typically delivered within 3 to 5 working days from the time your sample arrives at our laboratory. The analysis is performed by LC-MS/MS using a deuterium-labelled internal standard for accurate and reproducible quantification of ubiquinone.

Do statins affect CoQ10 levels?

Yes. Statins work by inhibiting HMG-CoA reductase, the rate-limiting enzyme in the mevalonate pathway. Because CoQ10 is synthesised via the same pathway, statin therapy can reduce endogenous CoQ10 production by up to 40%. This may contribute to statin-associated myopathy and fatigue. Monitoring CoQ10 levels is recommended for patients on long-term statin treatment to guide supplementation.

Which countries is this test available in?

Masdiag's CoQ10 test is available worldwide through our partner network. We currently serve healthcare professionals, wellness brands, and clinics in Europe, the United Kingdom, Asia, Australia, New Zealand, and the United States. Contact us to discuss testing services, white-label kits, or method transfer to your laboratory.

Interested in this method?

Whether you need testing services, method transfer, or white-label kit development — we'd love to hear from you.